DYKE-DAVIDOFF-MASSON SYNDROME-A Rare Cause of Cerebral Hemiatrophy in a 17-Years-Old Ethiopian Patient: A Case Report.

Journal: Ethiopian journal of health sciences

Volume: 29

Issue: 2

Year of Publication: 2019

Affiliated Institutions:  Department of Neurology, School of Medicine, College of Health Sciences, Addis Ababa University.

Abstract summary 

Dyke-Davidoff-Masson syndrome (DDMS) is a rare disease with unknown frequency, mainly presented with seizures, facial asymmetry, contralateral hemiparesis and mental retardation. Often, resulting from brain injury due to a multitude of causes, especially in early life, associated with birth asphyxia. Radiological findings include cerebral hemiatrophy/hypoplasia, calvarial thickening, and hyperpneumatization of the frontal sinuses.We report the case of a 17-year-old male patient who presented to Neurology Clinic with complaints of left side body weakness, walking difficulty and poorly controlled seizure for the past 6 years. Brain MRI revealed atrophy of the right cerebral hemisphere.Dyke-Davidoff-Masson syndrome should be suspected in any patients who present with classical features and brain imaging showing hemiatrophy. Early identification and treatment is important in such patients, as it can improve patients prognosis and quality of life.

Authors & Co-authors:  Ayele Biniyam Alemayehu BA Zewde Yared Zenebe YZ

Study Outcome 

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Statistics
Citations :  Verma R, Sahu R. Dyke-Davidoff-Masson syndrome. BMJ Case Reports. 2012 doi: 10.1136/bcr-2012-006729.
Authors :  2
Identifiers
Doi : 10.4314/ejhs.v29i2.16
SSN : 2413-7170
Study Population
Male
Mesh Terms
Adolescent
Other Terms
Cerebral hemiatrophy;Dyke-Davidoff-Masson syndrome;Magnetic resonance imaging;Seizure
Study Design
Case Study,Cross Sectional Study
Study Approach
Country of Study
Ethiopia
Publication Country
Ethiopia